Background: Kawasaki disease (KD) is a systemic vasculitis, of unknown etiology, that usually occurs in children between the ages of six months and five years. Patients at the extremes of ages rarely meet all the clinical criteria required for the diagnosis of KD. Atypical or incomplete presentation can lead to delayed diagnosis and treatment, resulting in a higher incidence of cardiac complications. Case Presentation: We describe the case of a 2-month-old female infant who was admitted to our clinic with persistent fever, generalized maculopapular rash and bilateral conjunctivitis. During hospitalization, she developed oral mucosa and extremity changes. On the 7th day from the onset of fever, the diagnosis of KD was established, and she received intravenous immunoglobulin therapy. The patient responded well to the treatment, presenting no cardiac complications. Conclusions: The presented case underscores that even very young infants can develop complete Kawasaki disease. It also highlights the importance of early identification and appropriate treatment in preventing coronary artery lesions.