Malanowska-Jarema, E.; Starczewski, A.; Osnytska, Y.; Krzyścin, M.; Sowińska-Przepiera, E.; Balzarro, M.; Rubilotta, E. Obstructed Hemivagina with Ipsilateral Renal Agenesis: A Challenging Case Report and a Management Flow Chart. J. Clin. Med.2023, 12, 7227.
Malanowska-Jarema, E.; Starczewski, A.; Osnytska, Y.; Krzyścin, M.; Sowińska-Przepiera, E.; Balzarro, M.; Rubilotta, E. Obstructed Hemivagina with Ipsilateral Renal Agenesis: A Challenging Case Report and a Management Flow Chart. J. Clin. Med. 2023, 12, 7227.
Malanowska-Jarema, E.; Starczewski, A.; Osnytska, Y.; Krzyścin, M.; Sowińska-Przepiera, E.; Balzarro, M.; Rubilotta, E. Obstructed Hemivagina with Ipsilateral Renal Agenesis: A Challenging Case Report and a Management Flow Chart. J. Clin. Med.2023, 12, 7227.
Malanowska-Jarema, E.; Starczewski, A.; Osnytska, Y.; Krzyścin, M.; Sowińska-Przepiera, E.; Balzarro, M.; Rubilotta, E. Obstructed Hemivagina with Ipsilateral Renal Agenesis: A Challenging Case Report and a Management Flow Chart. J. Clin. Med. 2023, 12, 7227.
Abstract
We present here a case of complex uterine anomaly – Obstructed HemiVagina with Ipsilateral Renal Agenesis (OHVIRA), also known as Herlyn-Werner-Wunderlich syndrome in a 13-year-old girl with the history of recurrent urinary tract infections (rUTI). In emergency room, trans-abdominal sonography revealed ovarian cyst and renal agenesis, without any suspicion of vaginal obstruction. This led to delay in the diagnosis of this uncommon anomaly. Finally, MRI findings confirmed the presence of OHVIRA syndrome.
As the congenital anomalies of kidney and urinary tract (CAKUT) are in almost one third of cases associated with genital malformations, urologist should carefully search for patients with rUTI. The patient underwent simultaneous laparoscopy and vaginoscopy, what was in our opinion the most appropriate therapeutic decision. In this article we are also going to discuss the role of laparoscopy in the management of OHVIRA syndrome as well as other surgical techniques described in the literature.
Keywords
obstructed vagina; OHVIRA syndrome; recurrent urinary tract infections (rUTI); congenital anomalies of kidney and urinary tract (CAKUT); renal agenesis; laparoscopic surgery in female adolescents
Subject
Medicine and Pharmacology, Obstetrics and Gynaecology
Copyright:
This is an open access article distributed under the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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